Congenital Desmoid Tumor of the Cheek: A Clinicopathological Case Report
نویسندگان
چکیده
OBJECTIVE Desmoid tumors are rare benign neoplasms of fibroblastic origin, frequently presenting in the abdomen of adult patients. Little is reported about clinical features and outcome of desmoid tumors appearing in infants and children, especially when they are located in the face. METHODS We report a girl with a desmoid tumor of her cheek, which was present at birth. RESULTS The tumor was treated by surgical excision, with no additional treatment, other than follow-up. No recurrence of the tumor was witnessed 15 months following surgical excision. SUMMARY Radical surgical treatment with tumor excision, sometimes accompanied by radiotherapy, is the current standard therapy for infantile desmoid tumors. Pharmacological treatment may be added in selected cases. These modalities may be challenging when desmoid tumors appear in the face because of risks of facial distortion and associated growth problems.
منابع مشابه
Huge Facial Desmoid Tumors with Neck Extension: A Case Report
Introduction: Desmoid tumors are very rare, benign fibrous neoplasms arise from the musculoaponeurotic structures throughout the body. Case Report: The patient was a seven-year old boy with a large mandibular mass growing over a period of six months. His CT-scan showed a large mass, 13 cm in diameter in the cheek area extending to the neck and trachea. Biopsy was compatible with desmoid fib...
متن کاملCongenital folliculosebaceous cystic hamartoma: A case report
Folliculosebaceous Cystic Hamartoma (FSCH) is a cutaneous hamartoma comprised of follicular, sebaceous and mesenchymal elements, and usually occurring during adulthood. Congenital and childhood presentations of this lesion are exceedingly rare. We describe herein a case of congenital FSCH on the midline and posterior region of the neck in a 1-year-old male infant and highlight the clinico...
متن کاملMultiple Congenital Epulis of the Mandibular Ridge: A Case Report
Congenital epulis is a very rare benign soft-tissue tumor of uncertain histogenesis, which is also known as “gingival granular cell tumor of the newborn”. It occurs almost exclusively as a single tumor along the alveolar ridge of the maxilla in newborn females. Although congenital epulis is strikingly similar to the more common adult granular cell tumor histologically, in contrast to the latter...
متن کاملCongenital Primitive Neuroectodermal Tumor (PNET) of the Orbit
Purpose: To report a case of the congenital primitive neuroectodermal tumor (PNET) of the orbit. Case Report: The patient was a 2-week-old neonate referred to the oculoplastic clinic with right eye proptosis from birth. The neonate was a full term with a history of difficult vaginal delivery. At an initial examination, the ecchymosis of the medial right upper lid was noted. At an initial CT sca...
متن کاملGastric Calcifying Fibrous Tumor Resembling Gastrointestinal Stromal Tumor: A Case Report
Calcifying fibrous tumor (CFT) is a rare mesenchymal tumor, affecting children and young adults with a predilection for the soft tissue and the abdominal cavity. CFT of the tubular gastrointestinal tract is very rare with less than 20 cases of gastric CFTs reported in English literature. This benign hypocellular fibrosclerotic calcifying lesion can resemble other spindle cell tumors particularl...
متن کامل